Synonyms

Cor triloculare biatriatum

Double-inlet left ventricle

Univentricular heart

UVH

Subtypes

Single ventricle with PS

Single ventricle with pulmonary stenosis

Single ventricle with transposition of great vessels

Single ventricle without PS

May Cause

Cardiomegaly in childhood

Complete atrioventricular canal

Heart failure in childhood

Left atrial enlargement

Right-to-left ventricular shunt

Systemic-to-pulmonary vascular shunt