Progressive sensorineural hearing loss - hypertrophic cardiomyopathy

Cytochrome c oxidase I (COX1) also known as mitochondrially encoded cytochrome c oxidase I (MT-CO1) is a protein that in humans is encoded by the MT-CO1 gene. In other eukaryotes, the gene is called COX1, CO1, or COI. Cytochrome c oxidase I is the main subunit of the cytochrome c oxidase complex. [Source: Wikipedia ]

Synonyms
Progressive neurosensory deafness - hypertrophic cardiomyopathy
Progressive sensorineural deafness - hypertrophic cardiomyopathy
OrphaNet reference
Progressive sensorineural hearing loss - hypertrophic cardiomyopathy 
May Cause
Hypertrophic cardiomyopathy
Progressive sensorineural deafness
Progressive neurosensory deafness - hypertrophic cardiomyopathy
Progressive sensorineural deafness - hypertrophic cardiomyopathy