Phakomatosis pigmentovascularis

Phakomatosis pigmentovascularis is a rare neurocutanous condition where there is coexistence of a capillary malformation (port-wine stain) with various melanocytic lesions, including dermal melanocytosis (Mongolian spots), nevus spilus, and nevus of Ota. Types Phakomatosis pigmentovascularis is subdivided into five types: Type 1 PWS + epidermal nevus Type 2 (most common): PWS + dermal melanocytosis +/- nevus anemicus Type 3: PWS + nevus spilus +/- nevus anemicus Type 4: PWS + nevus spilus + dermal melanocytosis +/- nevus anemicus Type 5: CMTC (Cutis marmorata telangiectatica congenita) + dermal melanocytosisThey all can contain capillary malformation. [Source: Wikipedia ]