Neurocutaneous melanosis

Neurocutaneous melanosis is a congenital disorder characterized by the presence of congenital melanocytic nevi on the skin and melanocytic tumors in the leptomeninges of the central nervous system. These lesions may occur in the amygdala, cerebellum, cerebrum, pons and spinal cord of patients. [Source: Wikipedia ]

Neurocutaneous melanocytosis
Rokitansky-van Bogaert syndrome
OrphaNet reference
Neurocutaneous melanocytosis 
May Cause
Congenital hydrocephalus
Neurocutaneous syndrome
Predominantly ectodermal phakomatosis