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Pulmonary atresia
Subtypes
Pulmonary atresia with intact ventricular septum
Transposition of great vessels with VSD and pulmonary atresia
Tricuspid atresia with pulmonary atresia
Tricuspid stenosis with pulmonary atresia
May Cause
Congenital heart disease with decreased pulmonary vascularity
Main pulmonary artery obstruction
Marked cyanosis in first week of life
Right atrial enlargement
Right ventricular enlargement
May Be Caused by
Robinow syndrome
Werner syndrome