Gamuts

Ebstein anomaly

Ebstein's anomaly is a congenital heart defect in which the septal and posterior leaflets of the tricuspid valve are displaced towards the apex of the right ventricle of the heart. It is classified as a critical congenital heart defect accounting for <1% of all congenital heart defects presenting in ≈1 per 200,000 live births. [Source: Wikipedia ]

OrphaNet reference
Ebstein malformation 
Subtypes
Ebstein anomaly with ASD
May Cause
Cardiomegaly in childhood
Generalized pulmonary arterial hypovascularity
Heart failure in childhood
Heart failure in the first month of life
Marked cyanosis in first week of life
Massive cardiomegaly
Rib notching
Right atrial enlargement
Right ventricular enlargement
Right-to-left atrial shunt
Third mogul sign
Tricuspid insufficiency
OrphaNet reference
Ebstein malformation 
Subtypes
Ebstein anomaly with ASD
May Cause
Cardiomegaly in childhood
Generalized pulmonary arterial hypovascularity
Heart failure in childhood
Heart failure in the first month of life
Marked cyanosis in first week of life
Massive cardiomegaly
Rib notching
Right atrial enlargement
Right ventricular enlargement
Right-to-left atrial shunt
Third mogul sign
Tricuspid insufficiency


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