CHORUS - home page


Collaborative Hypertext of Radiology

Respiratory system



pulmonary venolobar (scimitar) syndrome

  • always involves aplasia of one or more lobes of right lung

  • variably involves:
    • partial anomalous pulmonary venous return (scimitar-shaped vein)
      • usually drains to IVC; but portal vein, hepatic vein, RA possible
    • absent or small pulmonary artery perfusing abnormal lung segment
      • arterial supply from thoracic/abdominal aorta or celiac axis
    • anomalies of hemidiaphragm on affected side
    • anomalies of bony thorax or thoracic soft tissues

Richard Gunderman, MD  -  16 February 1995
Last updated:  1 October 2013


Related CHORUS documents:
scimitar syndrome
broncho-pulmonary sequestration
extralobar sequestration
intralobar sequestration
pleural fluid
white-matter disease


Copyright © 2013, Charles E. Kahn, Jr.