Collaborative Hypertext of Radiology
- rare syndrome consisting of:
- soft tissue tumors: keratoacanthoma, actinic keratosis, etc.
- internal malignancies (50% gastrointestinal, 25% genito-urinary)
- autosomal dominant inheritance
- high incidence of colonic polyps
- 120 reported cases
Brian Funaki, MD - 7 February 1995
Last updated: 1 October 2013
Copyright © 2013, Charles E. Kahn, Jr.