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Turcot syndrome
- autosomal recessive
- onset in teens
- GI-tract adenomas
- CNS tumors (esp. supratentorial glioblastoma) ==> death
- possible variant of Gardner syndrome
Cf: polyposis syndromes
Charles E. Kahn, Jr., MD - 2 February 1995
Last updated: 1 October 2013
Copyright © 2013, Charles E. Kahn, Jr.
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