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Nervous system

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ependymoma


  • frequency:
    • 6% of intracranial gliomas
    • 8-10% of childhood brain tumors
    • 63% of spinal intramedullary gliomas

  • age: supratentorial (any age); posterior fossa (<10 years)
  • a/w neurofibromatosis

  • location:
    • 4th ventricle (70% of intracranial gliomas)
    • lateral ventricle
    • 3rd ventricle
    • conus

  • findings:
    • sharply marginated isodense / slightly hyperdense mass
    • central necrosis (50%); calcification (50%)
    • enhancement (80%)
    • communicating hydrocephalus (100%) secondary to protein exudate clogging up resorption pathway
    • expansion through foramen of Luschka into CPA or caudad into cisterna magna (CHARACTERISTIC)
    • dissemination via CSF (10-33%)

  • DDx of cerebellar ependymoma:


Yong H. Hahn, MD  -  2 February 1995
Last updated:  1 October 2013


 

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gyral brain calcification

 

Copyright © 2013, Charles E. Kahn, Jr.