CHORUS
Collaborative Hypertext of Radiology
Multisystem entities
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scleroderma
progressive systemic sclerosis (PSS)
- hypertrophy then atrophy of collagen fibers
- 4-6th decade, M:F = 1:3
- bones
- punctate soft tissue ca++ (finger tips, shoulder, hips)
- acro-osteolysis (63%)
- intercarpal joint space narrowing (late)
- chest
- evident in 10-25%
- pulmonary fibrosis with diffuse reticulate infiltrate
- predominantly in lower lungs
- GI
see: CREST syndrome
Yong H. Hahn, MD - 2 February 1995
Last updated: 1 October 2013
Copyright © 2013, Charles E. Kahn, Jr.
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