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Gardner syndrome


  • autosomal dominant
  • adenomas --> colon Ca (tx: colectomy)
  • periampullary Ca

  • soft-tissue lesions
    • sebaceous cysts
    • subQ fibromas, leiomyomas, lipomas
  • bony lesions
    • osteomas (esp. in sinuses)
    • exostoses
    • cortical thickening
    • dental abnormalities (caries, extra teeth, odontomas)

see: polyposis syndromes


Charles E. Kahn, Jr., MD  -  2 February 1995
Last updated:  1 October 2013


 

Related CHORUS documents:
osteoma
polyposis syndromes
Turcot syndrome
familial polyposis coli
Peutz-Jeghers syndrome
Cronkhite-Canada syndrome

 

Copyright © 2013, Charles E. Kahn, Jr.