CHORUS
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Gardner syndrome
- autosomal dominant
- adenomas --> colon Ca (tx: colectomy)
- periampullary Ca
- soft-tissue lesions
- sebaceous cysts
- subQ fibromas, leiomyomas, lipomas
- bony lesions
- osteomas (esp. in sinuses)
- exostoses
- cortical thickening
- dental abnormalities (caries, extra teeth, odontomas)
see: polyposis syndromes
Charles E. Kahn, Jr., MD - 2 February 1995
Last updated: 1 October 2013
Copyright © 2013, Charles E. Kahn, Jr.
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