
CHORUS
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Nervous system
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Schilder syndrome
sudanophilic leukodystrophy
- males (2:1), onset prepuberty
- rapidly progressive demyelinating disease
- weakness --> paralysis
- apathy --> stupor
- death usually in months
- occipital + temporal most severely affected
Charles E. Kahn, Jr., MD - 2 February 1995
Last updated: 1 October 2013
Copyright © 2013, Charles E. Kahn, Jr.
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