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Schilder syndrome


    sudanophilic leukodystrophy
  • males (2:1), onset prepuberty
  • rapidly progressive demyelinating disease
    • weakness --> paralysis
    • apathy --> stupor
    • death usually in months

  • occipital + temporal most severely affected


Charles E. Kahn, Jr., MD  -  2 February 1995
Last updated:  1 October 2013


 

Related CHORUS documents:
demyelinating disease
disseminated necrotizing leukoencephalopathy
Binswanger disease
central pontine myelinolysis
acute disseminated encephalomyelitis
dysmyelinating disease

 

Copyright © 2013, Charles E. Kahn, Jr.