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Liver and biliary system

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portal hypertension: classification


PRESINUSOIDAL
  • extrahepatic:
    • portal vein obstruction (extrinsic compression, phlebitis, OC, coagulopathy, tumor invasion, pancreatitis, neonatal omphalitis)
    • dynamic: traumatic/neoplastic arterioportal fistula
    • segmental portal HTN: splenic/SMV occlusion
  • intrahepatic (obstruction of portal venules):
    • congenital hepatic fibrosis
    • primary biliary cirrhosis
    • sarcoid
    • myelofibrosis
    • schistosomiasis
    • idiopathic noncirrhotic fibrosis
    • Wilson disease
    • reticuloendotheliosis
    • Felty syndrome
    • chronic malaria
    • toxic fibrosis (arsenic, copper, PVC vapors)
SINUSOIDAL POSTSINUSOIDAL


Yong H. Hahn, MD  -  2 February 1995
Last updated:  1 October 2013


 

Related CHORUS documents:
portal hypertension
esophageal varices
Budd-Chiari syndrome
primary biliary cirrhosis
splenomegaly
sarcoidosis

 

Copyright © 2013, Charles E. Kahn, Jr.