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CHORUS

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Multisystem entities

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Sjogren syndrome


chronic systematic inflammatory disorder of unknown etiology characterized by dryness of mucous membranes

  • primary Sjogren syndrome:
    • without underlying autoimmune disease
    • recurrent parotitis in children
    • sicca syndrome (xerophthalmia and xerostomia)

  • secondary Sjogren syndrome:
    • connective tissue diseases (RA, SLE, PSS, psoriasis, etc)
    • lymphoprolifertive disorders (lymphocytic interstitial pneumonitis, pseudolymphoma, lymphoma, Waldenstrom macroglobulinemia)

Findings:
  • CXR: reticulododular pattern, patchy consolidation/atelactisis, pneumonitis, +/- pleural effusion
  • U/S: multiple scattered parotid cysts bilaterally
  • enlarged lacrimal glands


Yong H. Hahn, MD  -  2 February 1995
Last updated:  1 October 2013


 

Related CHORUS documents:
tibio-talar slant
Wegener granulomatosis
gallbladder carcinoma
lacrimal gland enlargement
Wolman disease
orbital pseudotumor

 

Copyright © 2013, Charles E. Kahn, Jr.