CHORUS
Collaborative Hypertext of Radiology
Multisystem entities
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Sjogren syndrome
chronic systematic inflammatory disorder of unknown etiology
characterized by dryness of mucous membranes
- primary Sjogren syndrome:
- without underlying autoimmune disease
- recurrent parotitis in children
- sicca syndrome (xerophthalmia and xerostomia)
- secondary Sjogren syndrome:
- connective tissue diseases (RA, SLE, PSS, psoriasis, etc)
- lymphoprolifertive disorders (lymphocytic interstitial pneumonitis,
pseudolymphoma, lymphoma, Waldenstrom macroglobulinemia)
Findings:
- CXR: reticulododular pattern, patchy consolidation/atelactisis,
pneumonitis, +/- pleural effusion
- U/S: multiple scattered parotid cysts bilaterally
- enlarged lacrimal glands
Yong H. Hahn, MD - 2 February 1995
Last updated: 1 October 2013
Copyright © 2013, Charles E. Kahn, Jr.
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