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endocardial fibroelastosis


  • unknown etiology
  • diffuse thickening of endocardium
  • few live > 2 yrs

  • limited to LEFT chambers in 80%

  • causes restrictive cardiomyopathy


Charles E. Kahn, Jr., MD  -  2 February 1995
Last updated:  1 October 2013


 

Related CHORUS documents:
restrictive cardiomyopathy
hypoplastic left heart syndrome
cardiomyopathy
neonatal heart failure
congenital cardiomyopathy
subvalvular aortic stenosis

 

Copyright © 2013, Charles E. Kahn, Jr.