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Turcot syndrome


  • autosomal recessive
  • onset in teens

  • GI-tract adenomas
  • CNS tumors (esp. supratentorial glioblastoma) ==> death

  • possible variant of Gardner syndrome

Cf: polyposis syndromes


Charles E. Kahn, Jr., MD  -  2 February 1995
Last updated:  1 October 2013


 

Related CHORUS documents:
Gardner syndrome
polyposis syndromes
familial polyposis coli
Cronkhite-Canada syndrome
Peutz-Jeghers syndrome
Cowden syndrome

 

Copyright © 2013, Charles E. Kahn, Jr.