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Respiratory system

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cystic fibrosis


  • probably autosomal recessive
  • common in whites, 1:2000
  • clinically: resp. disease, GI symptoms

complications:
  • bronchiectasis
  • pneumothorax
  • hemoptysis
  • lobar atelectasis
  • pulmonary HTN
  • cor pulmonale {normal-size heart may represent CMG}
  • large, opacified sinuses

DDx: Riley-Day syndrome


Charles E. Kahn, Jr., MD  -  2 February 1995
Last updated:  1 October 2013


 

Related CHORUS documents:
bronchiectasis
Riley-Day syndrome
Kartagener syndrome
echogenic pancreas
Chagas disease
chronic granulomatous disease of childhood

 

Copyright © 2013, Charles E. Kahn, Jr.