CHORUS

Collaborative Hypertext of Radiology

Nervous system

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moyamoya disease

• affecting distal ICA at bifurcation into its branches (ant. 2/3 of circle of Willis)
• usually involving both hemispheres

• etiology: unknown
• age: predominantly in children and young adults.

clinical:

• headaches
• behavioral disturbances
• recurrent hemiparetic attacks

radiographic findings:

• large network of vessels in BG (puff of smoke) and upper brainstem fed by
  • basilar a.
  • ACA
  • MCA (dilatation of lenticulo-striates and ant. choroidal a.)
• anastomosis between leptomeningeal and dural meningeal arteries

complication: subarachnoid hemorrhage (occasionally)

Related CHORUS documents: acute spinal cord compression Cowden syndrome progressive supranuclear palsy (Steele-Richardson-Olszewski syndome) leukodystrophy hypoplastic left heart syndrome reflex sympathetic dystrophy

Copyright © 2013, Charles E. Kahn, Jr.