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Erdheim-Chester disease


rare lipidosis

  • age: 50-70y

  • long bones invariably affected in the diaphysis and metaphysis with:
    • patchy or diffuse increase in density
    • coarsened trabecular pattern
    • medullary sclerosis
    • cortical thickening


Brian Funaki, MD  -  6 February 1995
Last updated:  1 October 2013


 

Related CHORUS documents:
Hand-Schueller-Christian disease
Chopart fracture-dislocation
rheumatoid arthritis: joint manifestations

 

Copyright © 2013, Charles E. Kahn, Jr.