CHORUS

Collaborative Hypertext of Radiology

Cardiovascular system

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hypoplastic left heart syndrome

• aortic valve atresia
• hypoplastic ascending aorta
• hypoplastic/atretic mitral valve
• endocardial fibroelastosis

• 25% of cardiac deaths in 1st week of life
• prognosis if untreated: 100% fatal by 6 weeks

• pulmonary venous return is diverted from LA to RA through ASD
• RV supplies pulmonary artery, ductus arteriosus, descending aorta (antegrade flow), aortic arch, ascending aorta, coronary circulation (retrograde flow)
• leads to RV work overload and CHF

• Norwood procedure (palliative) - three stage surgery that results in the RA feeding the pulmonary circulation and the RV feeding the systemic circulation.
• transplant

Related CHORUS documents: neonatal heart failure endocardial fibroelastosis abnormal heart chamber dimensions leukodystrophy restrictive cardiomyopathy reflex sympathetic dystrophy

Copyright © 2013, Charles E. Kahn, Jr.