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Liver and biliary system

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primary sclerosing cholangitis


  • idiopathic
    • a/w IBD (50%), usually UC
  • M > F
  • peak age 20-30 y/o

  • chronic inflammation + fibrosis of all bile ducts
  • stricture, obstruction, abscess ("string of beads")
  • intramural pseudo-diverticula

  • cholangioCa (10%!!)
    • dilatation proximal to stricture may signal Ca

DDx:


Charles E. Kahn, Jr., MD  -  2 February 1995
Last updated:  1 October 2013


 

Related CHORUS documents:
cholangiocarcinoma
Klatskin tumor
Clonorchis sinensis
primary biliary cirrhosis
Oriental cholangio-hepatitis
Courvoisier phenomenon

 

Copyright © 2013, Charles E. Kahn, Jr.