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Collaborative Hypertext of Radiology


Musculoskeletal system

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basal cell nevus syndrome


Gorlin syndrome

  • autosomal dominant

  • multiple nevoid basal-cell carcinomas
  • odontogenic keratocysts (OKCs)
  • rib + vertebral anomalies
  • short metacarpal(s)


Charles E. Kahn, Jr., MD  -  2 February 1995
Last updated:  1 October 2013


 

Related CHORUS documents:
short metacarpals
prune belly (Eagle-Barrett) syndrome
Wilms tumor
pearl necklace gallbladder
osteochondroma (exostosis)
hereditary exostosis (osteochondromatosis)

 

Copyright © 2013, Charles E. Kahn, Jr.