CHORUS
Collaborative Hypertext of Radiology
Kidney
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Potter syndrome
- I
- autosomal recessive ("infantile") polycystic disease
- "microscopic" (1-mm) cysts
- US: +/- increased echo, no gross cysts
- II
- multicystic dysplastic kidney ("renal dysplasia")
- US: multiple cysts, usually unilateral
- III
- autosomal dominant ("adult") polycystic disease
- usually not present until adult life
- US: multiple cysts
- renal agenesis
associated with:
Charles E. Kahn, Jr., MD - 2 February 1995
Last updated: 1 October 2013
Copyright © 2013, Charles E. Kahn, Jr.
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