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CHORUS

Collaborative Hypertext of Radiology


Multisystem entities

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MEN-2 (Sipple) syndrome


    multiple endocrine neoplasia (MEN) syndrome

  • medullary thyroid Ca
    • usually multifocal; mets --> local nodes, lung, liver
    • usually calcify in liver

  • pheochromocytoma
    • almost always bilateral

  • parathyroid hyperplasia
    • may be 2' to calcitonin secreted by medullary thyroid Ca

inconstant feature:
  • adrenal cortical hyperplasia


Charles E. Kahn, Jr., MD  -  2 February 1995
Last updated:  1 October 2013


 

Related CHORUS documents:
pheochromocytoma
MEN-3 (Schimke, marfanoid) syndrome
multiple endocrine neoplasia (MEN)
MEN-1 (Wermer) syndrome
von Hippel-Lindau syndrome
Marfan syndrome

 

Copyright © 2013, Charles E. Kahn, Jr.