
CHORUS
Collaborative Hypertext of Radiology
Respiratory system
About CHORUS
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cystic fibrosis
- probably autosomal recessive
- common in whites, 1:2000
- clinically: resp. disease, GI symptoms
complications:
- bronchiectasis
- pneumothorax
- hemoptysis
- lobar atelectasis
- pulmonary HTN
- cor pulmonale {normal-size heart may represent CMG}
- large, opacified sinuses
DDx: Riley-Day syndrome
Charles E. Kahn, Jr., MD - 2 February 1995
Last updated: 1 October 2013
Copyright © 2013, Charles E. Kahn, Jr.
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