bullous diseases of esophagus

epidermolysis bullosa dystrophica
- autosomal recessive
- presents in infancy or later life
- epidermal-dermal separation
- +/- anal strictures
- Rx: conservative, soft diet
benign mucous membrane (cicatricial) pemphigoid
- not "pemphigus vulgaris"
- not bullous pemphigoid
- females (2:1), elderly

Charles E. Kahn, Jr., MD - 2 February 1995
Last updated: 1 October 2013