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Nervous system

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Alexander disease


dysmyelinating disease
  • rare, sporadic
  • usually presents in 1st year
  • megalencephaly: gradual enlargement of head
  • retardation, convulsion, spasticity

CT findings:
  • decreased density of white matter
  • frontal lobe predominance
  • +/- dilated lateral ventricles

Dx: brain bx


Charles E. Kahn, Jr., MD  -  2 February 1995
Last updated:  1 October 2013


 

Related CHORUS documents:
leukodystrophy
dysmyelinating disease
adrenoleukodystrophy
Pelizaeus-Merzbacher syndrome
globoid cell (Krabbe) leukodystrophy
spongy degeneration (Canavan disease)

 

Copyright © 2013, Charles E. Kahn, Jr.